Turkish Journal of Physical Medicine and Rehabilitation 2012 , Vol 58 , Num 2

Pulmonary Amyloidosis Mimicking Interstitial Lung Disease in a Patient With Polymyozitis

Asena Gökçay 1 ,Metin Işık 1 ,Meral Çalgüneri 1
1 Hacettepe Üniversitesi Tıp Fakültesi, Erişkin Hastanesi, Romatoloji, Ankara, Türkiye DOI : 10.4274/tftr.55706

Primary pulmonary amyloidosis is a localized type of amyloidosis which usually presents with parenchymal nodules, diffuse alveolar damage, or submucosal deposits in the airways. Polymyozitis is an inflammatory autoimmune myopathy characterized by symmetric weakness of the limb girdle and anterior neck muscles. Nearly 80-90% of cases with polymyositis are successfully treated with steroid and cyclophosphamide combination therapies. Polymyozitis also cause secondary interstitial lung disease and the radiological findings of these two diseases may not be easily discriminated from each other. 

Keywords : Polymyozitis, interstitial lung disease, primary pulmonary amyloidosis