Turkish Journal of Physical Medicine and Rehabilitation 2017 , Vol 63 , Num 2

Coexistence of familial Mediterranean fever and Behçet’s disease: a case report

Tuba Güler 1 ,Yeşim Garip 2 ,Fulya Dörtbaş 3 ,Ayşe Aslıhan Karcı 4 ,Nurşad Çifçi 5
1 Department of Physical Medicine and Rehabilitation, Derince Training and Research Hospital, Kocaeli, Turkey
2 Department of Physical Medicine and Rehabilitation, Başak Medical Center, Ankara, Turkey
3 Department of Rheumatology, Derince Training and Research Hospital, Kocaeli, Turkey
4 Department of Ophtalmology, Derince Training and Research Hospital, Kocaeli, Turkey
5 Department of Dermatology, Derince Training and Research Hospital, Kocaeli, Turkey
DOI : 10.5606/tftrd.2017.72681 Behçet’s disease (BD) is a chronic, multi-systemic vasculitis, characterized by a triad of recurrent aphthous stomatitis, genital aphthae, and uveitis. It is common in the Eastern Mediterranean, Middle East, and Eastern Asian countries. Familial Mediterranean fever (FMF) is an autosomal recessive autoinflammatory disorder, which is common seen in the Turkish, Armenian, Arabic, and Sephardic Jewish populations. It is characterized by recurrent episodes of fever, peritonitis, pleuritis, arthritis, and erysipelas-like skin lesions. Behçet’s disease and FMF have common clinical features and geographic distribution. Herein, we present a 19-year-old female patient with coexistence of FMF and BD in the light of literature data. Keywords : Behçet's disease; Familial Mediterranean fever; hereditary autoinflammatory diseases