Turkish Journal of Physical Medicine and Rehabilitation 2004 , Vol 50 , Num 6

Primer Hipertrofik Osteoartropati (Pakidermoperiostozis)

Bülent Hazneci 1 ,İltekin Duman 2 ,Arif Kenan Tan 3 ,Kemal Dinçer 1 ,Tunç Alp Kalyon 4
1 Gülhane Askeri Tıp Akademisi, Fiziksel Tıp ve Rehabilitasyon Anabilim Dalı, Ankara
2 Gülhane Askeri Tıp Akademisi, Fiziksel Tıp ve Rehabilitasyon Anabilim Dalı, TSK Rehabilitasyon ve Bakım Merkezi, Ankara, Türkiye
3 GATA Fiziksel Tıp ve Rehabilitasyon Anabilim Dalı, Ankara
4 T.C. Sağlık Bakanlığı Akupunktur Bilim Komisyonu Üyesi, Ankara

There are many certain sistemic diseases that may be associated with clubbing of fingers. In primary (idiopathic) hypertrophic osteoarthropathy (HOA) which is a rare condition, there are marked skin signs in addition to clubbing. For this reason, the definition of primary HOA as pachydermoperiostosis is largely accepted. In patients with primary HOA, the hypertrophy of the skin is so marked that, thickening of facial folds and appearance of leonine face may suggest acromegaly. In this article a patient with leonine face due to pachydermoperiostosis is presented and discussed along with literature review.

Keywords : Finger clubbing, primer hypertrophic osteoarthropathy, pachydermoperiostosis